BC43.6Ангилал

Arrhythmogenic ventricular cardiomyopathy

Тодорхойлолт

Arrhythmogenic ventricular cardiomyopathy is a cardiomyopathy characterised by myocardial cell loss with partial or total replacement of right ventricular muscle by adipose and fibrous tissue, beginning subepicardially to become transmural in time, sparing the papillary muscles and trabeculae, and often associated with aneurysms particularly of the right ventricular outflow tract. There is progressive systolic impairment with ventricular dilation and marked propensity for ventricular arrhythmias of right, as well as left, ventricular origin. Classically a disease of the right ventricle, more recent evidence suggests left ventricular involvement to a varying extent in up to 75% of cases, as well as isolated left ventricular disease.

Индексийн нэр томьёо Index terms · 17

Arrhythmogenic ventricular cardiomyopathyarrhythmogenic ventricular dysplasiaArrhythmogenic ventricular cardiomyopathy due to desmosomal mutationArrhythmogenic ventricular cardiomyopathy with right ventricular dominancearrhythmogenic right ventricular dysplasiaarrhythmogenic right ventricular cardiomyopathyARVC - [Arrhythmogenic right ventricular cardiomyopathy]ARVD - [Arrhythmogenic right ventricular dysplasia]Familial isolated arrhythmogenic right ventricular dysplasiaNaxos diseaseKeratosis palmoplantaris with arrhythmogenic cardiomyopathyArrhythmogenic ventricular cardiomyopathy with left ventricular dominancearrhythmogenic left ventricular dysplasiaarrhythmogenic left ventricular cardiomyopathyWoolly hair – palmoplantar keratoderma – dilated cardiomyopathyCarvajal-Huerta syndromeCarvajal syndrome

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